Successful Lung Transplantation for Pulmonary Disease Associated With Erdheim-Chester Disease.

Successful Lung Transplantation for Pulmonary Disease Associated With Erdheim-Chester Disease. Ann Thorac Surg. 2017 Jul;104(1):e13-e15 Authors: Hashimoto K, Miyoshi K, Mizutani H, Otani S, Sugimoto S, Yamane M, Oto T Abstract A 53-year-old man with pulmonary fibrosis associated with Erdheim-Chester disease achieved long-term survival after lung transplantation. Major clinical manifestations included lung and bone injuries, and other vital organs were functionally unaffected by the disease. After a careful observation for the disease progression, he underwent bilateral deceased-donor lung transplantation. He has returned to his normal social life and is doing well without recurrence of Erdheim-Chester disease in the lung allograft or progression in other organs 5 years after transplant. Lung transplantation is a potentially reasonable treatment option for Erdheim-Chester disease involving the lungs if the functions of other vital organs remain stable. PMID: 28633251 [PubMed - in process]
Source: The Annals of Thoracic Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Tags: Ann Thorac Surg Source Type: research