European Glaucoma Society Terminology and Guidelines for Glaucoma, 4th Edition - Chapter 2: Classification and terminology * Supported by the EGS Foundation: Part 1: Foreword; Introduction; Glossary; Chapter 2 Classification and Terminology

2Classification and Terminology2.1- Primary Congenital Forms/Childhood Glaucomas Primary congenital glaucoma is a rare disease but has a major impact on the child’s development and quality of life over his/her whole life span. Early diagnosis and appropriate therapy can make a huge difference in the visual outcome and can prevent lifelong disability. Surgical treatment is always necessary1, 2 [I,C]. 2.1.1Primary congenital glaucoma (PCG): from birth to >2 years of life Neonatal or newborn onset (0-1 month) Infantile onset (>1 until 24 months) Late onset or late recognized (>2 years) Spontaneously non-progressing cases with normal IOP but typical signs of PCG may be classified as PCG Etiology: Angle dysgenesis is caused by incomplete development of the trabecular meshwork before and/or after birth. Strong monogenetic influence. Heredity shows recessive inheritance with variable penetrance in most cases or is sporadic. Specific...
Source: British Journal of Ophthalmology - Category: Opthalmology Tags: Open access Supplementary pages Source Type: research