Diplopia with Dural Fibrotic Thickening

Idiopathic hypertrophic pachymeningitis is a rare disorder of diffuse thickening of the cranial or spinal dura matter without an identifiable cause. Most common in adult males, idiopathic hypertrophic pachymeningitis typically presents with headache with or without varied associated focal neurologic deficits and findings of dural enhancement on MRI in a linear, nodular or combined pattern. As it is felt to be an autoimmune disorder, treatment with high dose corticosteroids is typically recommended, and without intervention, the course is usually progressive.

Source: Seminars in Pediatric Neurology - April 14, 2017 Category: Neurology Authors: Brittany Brand, Dave Somers, Blake Wittenberg, Jessica Gautreaux, Stephen Deputy Source Type: research