What Treatment is Available for Lymphatic Malformations?

Discussion Vascular malformations including those of the arterial, venous and lymphatic systems are due to an arrest of the normal process of angiogenesis, vasculogenesis and remodeling of the vessels. They are not tumors and need to be differentiated from benign and malignant vascular lesions. They occur in 1.5% of the population with 90% present at birth. The nomenclature of congenital lymphatic malformations can be confusing. They can be present in any location and may have mixed elements within them (i.e. lymphatic and venous, lymphatic and arterial, etc.) and different structural components such as dilatation or hyperplasia. Thus people will use different wording that can be ambiguous or incorrect. Lymphatic malformations and problems can be acquired also usually secondary to trauma or surgery with problems arising in the adjacent tissues. An example in the adult population is lymphedema after breast surgery and in the pediatric population is a chylothorax after congenital open-heart surgery. Cystic hygromas or true congenital lymphatic cysts, are lymphatic malformations that have normal development of the lymphatic system but do not establish the normal communication with the venous system. These can occur anywhere in the body but occur often in the head and neck, many times on the left side. Some cystic hygromas are associated with chromosomal abnormalities particularly Turner’s syndrome. Lymphatic malformations may be seen in various syndromes including Down,...
Source: PediatricEducation.org - Category: Pediatrics Authors: Tags: Uncategorized Source Type: news