Long-term outcome after treatment of pulmonary atresia with ventricular septal defect: nationwide study of 109 patients born in 1970-2007 [CONGENITAL]

CONCLUSIONS These findings show that achievement of repair and initial size of true central pulmonary arteries affect survival of patients with PA + VSD. Although the overall survival of patients with MAPCAs showed no difference compared with simple PA + VSD patients, they had a higher risk of remaining palliated. However, palliative surgery may have a role in treatment of PA + VSD because the size of pulmonary arteries increased after placement of systemic–pulmonary artery shunt. In addition, subtotal repair by a RV–pulmonary artery connection and septal fenestration improved survival over extracardiac palliation.
Source: European Journal of Cardio-Thoracic Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Tags: Mechanical Circulatory Assistance CONGENITAL Source Type: research