Device Therapy in the Setting of Long QT Syndrome

Publication date: Available online 8 July 2015 Source:Cardiac Electrophysiology Clinics Author(s): Troy Rhodes , Raul WeissTeaser Congenital long QT syndrome (LQTS) is an inherited disorder of myocardial repolarization characterized by prolongation of the QT interval associated with life-threatening polymorphic ventricular tachycardia. The treatment of congenital LQTS involves antiadrenergic therapies: β-blockers and surgical left cardiac sympathetic denervation (LCSD) to decrease sympathetic input to the heart, cardiac pacing, and implantable cardioverter-defibrillator (ICDs). Although this article focuses on the role of device therapy for the treatment of LQTS, it also discusses the role of β-blockers and LCSD because they are concomitant with device therapy. After implantation, programming should be optimized to minimize the risk for inappropriate ICD therapies.
Source: Cardiac Electrophysiology Clinics - Category: Cardiology Source Type: research